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dravet syndrome

Medical Definition

An autosomal dominant form of early infantile epileptic encephalopathy, caused by mutation(s) in the scn1a gene, encoding sodium channel protein type 1 subunit alpha.

Wikipedia Summary

Dravet syndrome (DS), previously known as severe myoclonic epilepsy of infancy (SMEI), is an autosomal dominant genetic disorder which causes a catastrophic form of epilepsy, with prolonged seizures that are often triggered by hot temperatures or fever. It is very difficult to treat with anticonvulsant medications...
Related Codes (3)
Code
Description
Billable
Details
G40.83Dravet syndrome
G40.833Dravet syndrome, intractable, with status epilepticus
G40.834Dravet syndrome, intractable, without status epilepticus

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